Publication: Liver transplantation because of acute liver failure due to heme arginate overdose in a patient with acute intermittent porphyria
Liver transplantation because of acute liver failure due to heme arginate overdose in a patient with acute intermittent porphyria
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Frei, P., Minder, E. I., Corti, N., Muellhaupt, B., Geier, A., Adams, H., Dutertre, J.-P., Rudiger, A., Dutkowski, P., Maggiorini, M., & Ganter, C. C. (2012). Liver transplantation because of acute liver failure due to heme arginate overdose in a patient with acute intermittent porphyria. Case Reports in Gastroenterology, 6, 190–196. https://doi.org/10.1159/000338354
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In acute attacks of acute intermittent porphyria, the mainstay of treatment is glucose and heme arginate administration. We present the case of a 58-year-old patient with acute liver failure requiring urgent liver transplantation after erroneous 6-fold overdose of heme arginate during an acute attack. As recommended in the product information, albumin and charcoal were administered and hemodiafiltration was started, which could not prevent acute liver failure, requiring super-urgent liver transplantation after 6 days. The explanted li
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Frei, P., Minder, E. I., Corti, N., Muellhaupt, B., Geier, A., Adams, H., Dutertre, J.-P., Rudiger, A., Dutkowski, P., Maggiorini, M., & Ganter, C. C. (2012). Liver transplantation because of acute liver failure due to heme arginate overdose in a patient with acute intermittent porphyria. Case Reports in Gastroenterology, 6, 190–196. https://doi.org/10.1159/000338354